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Ophthalmology and Visual Sciences

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Boston Keratoprosthesis (KPro) for congenital aniridia

Contributor: Jesse Vislisel, MD

Photographers:  Tracy Aly, CRA and Brice Critser, CRA

Congenital aniridia is a hereditary disease most commonly with autosomal dominant inheritance.  These slit lamp photographs of a 12-year-old with congenital aniridia (Fig. 1 A, B) show conjunctivalization of the left cornea due to stem cell deficiency and a central corneal scar.  There is iris hypoplasia in both eyes.  The patient has a congenital cataract in the right eye and is aphakic in the left eye after having undergone cataract surgery.  The cataract and corneal scars are more easily demonstrated on retroillumination.  Also note the visible inferior border of the crystalline lens and zonules in the right eye, a feature not visible in individuals with normal irides.  The lower photos (Fig. 2) show the appearance of the left eye after placement of a Boston Keratoprosthesis (KPro).  Please see the related case report for more information about congenital aniridia.

Figure 1.

Slit lamp photographs of another patient with congenital aniridia. There is conjunctivalization of the left cornea due to stem cell deficiency and a central corneal scar. There is iris hypoplasia in both eyes. Slit lamp photographs of another patient with congenital aniridia. There is conjunctivalization of the left cornea due to stem cell deficiency and a central corneal scar. There is iris hypoplasia in both eyes.
The cataract and corneal scars are demonstrated on retroillumination The cataract and corneal scars are demonstrated on retroillumination

Figure 2. Postoperative Appearance:

Postoperative appearance of the patient in Figure 3 after placement of a Boston keratoprosthesis (KPro).

Postoperative appearance of the patient in Figure 3 after placement of a Boston keratoprosthesis (KPro).

Postoperative appearance of the patient in Figure 3 after placement of a Boston keratoprosthesis (KPro).


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last updated: 05/11/2015
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