Retinal hemangioblastoma associated with Von-Hippel Lindau syndrome
Contributor: William Flanary, MD
Photographer: Toni Venckus, CRA
This patient is a 76-year-old woman with Von-Hippel Lindau syndrome. In additional to the many small hemangiomas that were previously treated, she had a large superotemporal hemangioma that was treated more than 10 years prior with cryotherapy and photocoagulation. On follow up, she is found to have a moderately sized hemangioma just inferior to the largest previously treated lesion. There is a second, early hemangioma superonasal to the large chorioretinal scar seen on the montage photo. Capillary hemangiomas in the peripheral retina can often be observed as they are known to spontaneously regress or remain stable for years. Commonly used treatment modalities include argon laser photocoagulation, cryotherapy, and photodynamic therapy. Some studies suggest a benefit to using anti-VEGF as an adjunctive therapy.
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