EyeRounds Online Atlas of Ophthalmology

Contributor:
William Charles Caccamise Sr,MD, Retired Clinical Asst Prof of Ophthal. U.of Rochester School of Medicine & Dentistry

Category: Neuro-ophthalmology
Diagnosis: Sturge-Weber Syndrome: a bulbar manifestation

Image Comments:

A bulbar " can of worms " bloodvessels in a patient with Sturge-Weber syndrome. In the photo, the facial vascularity is seen as vague speckling of the skin of the lid. In reality, the patient - a law school graduate - has a markedly disfiguring facial involvement that relegates him to law library work where he does not have to face the public. He is receiving laser treatment from a dermatologist for his right facial lesions. Reference: Stedman's Medical Dictionary:" Sturge-Weber syndrome, in full, a triad: congenital cutaneous angioma ( flame nevus) in the distribution of the trigeminal nerve, usually unilateral, homolateral meningeal angioma with intracranial calcification and neurologic signs, and angioma of choroid, often with secondary glaucoma; incomplete forms of the syndrome may exhibit any two of the major features in variable degree."

 

 

---

NO ONE MAY USE THESE PHOTOGRAPHS FOR PUBLICATIONS OR FINANCIAL GAIN WITHOUT WRITTEN AUTHORIZATION FROM THE CONTRIBUTING AUTHOR.